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Hemidystonia and Hemichoreoathetosis as an Initial Manifestion of Moyamoya Disea

 Chul Hyoung Lyoo  ;  Seung Hun Oh  ;  Jin-Yang Joo  ;  Tae-Sub Chung  ;  Myung Sik Lee 
 Archives of Neurology, Vol.57(10) : 1510-1512, 2000 
Journal Title
 Archives of Neurology 
Issue Date
Adult ; Athetosis/diagnosis* ; Athetosis/etiology ; Brain/metabolism ; Brain/pathology ; Chorea/diagnosis* ; Chorea/etiology ; Dystonia/diagnosis* ; Dystonia/etiology ; Female ; Humans ; Magnetic Resonance Imaging ; Moyamoya Disease/complications* ; Moyamoya Disease/diagnosis* ; Severity of Illness Index ; Tomography, Emission-Computed
OBJECTIVE: To describe hemidystonia and hemichoreoathetosis in an adult patient with moyamoya disease without a previous history of cerebrovascular accident. DESIGN: Case report. SETTING: Tertiary care center. PATIENT: A 22-year-old woman suddenly developed dystonic spasms in her left hand and left foot after a severe emotional stress. The dyskinesia gradually subsided over the next 4 months. Five months after the onset, she suddenly developed choreoathetoid movement in her right hand and right foot. MAIN OUTCOME AND RESULTS: The patient had both somatic and cortical sensory deficits in the right hand and right foot. Magnetic resonance imaging of the brain showed an infarction at the right putamen and lesions involving the right frontal lobe and the left frontotemporoparietal lobe. Magnetic resonance cerebral angiography showed severe stenoses of both internal carotid arteries at the supraclinoid portion and numerous collateral vessels, compatible with moyamoya disease. Single photon emission tomography of the brain showed hypoperfused areas at the right frontal and left frontotemporoparietal lobes. The choreoathetosis of the right limbs improved markedly, along with improvement of sensory deficits. CONCLUSIONS: To our knowledge, this is the first report of an adult patient presenting with hemidystonia and hemichoreoathetosis as the initial manifestations of moyamoya disease. Arch Neurol. 2000;57:1510-1512
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1. College of Medicine (의과대학) > Dept. of Radiology (영상의학교실) > 1. Journal Papers
1. College of Medicine (의과대학) > Dept. of Neurosurgery (신경외과학교실) > 1. Journal Papers
Yonsei Authors
Chung, Tae Sub(정태섭)
Joo, Jin Yang(주진양)
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