Surgical and wound management for hand-localized kaposiform hemangioendothelioma: a case report

Abstract

Kaposiform hemangioendothelioma (KHE) is a rare, aggressive vascular tumor predominantly seen in children. It can infiltrate the deeper soft tissues and is clinically marked by erythematous to violet plaques, sometimes associated with the Kasabach-Merritt phenomenon. A male neonate presented with a substantial mass on the dorsum of his left hand. Surgical excision on the 8th day after birth identified the tumor as KHE, without evidence of Kasabach-Merritt syndrome. Two additional operations were performed over the following year to address contractures and restore finger function. At a 6-month follow-up, the patient showed no significant functional impairment. KHE poses unique clinical challenges due to its aggressive nature. This case highlights the need for prompt surgical intervention, given the tumor’s size and location. Managing KHE requires a rapid diagnosis and intervention, particularly in functionally critical areas, to ensure optimal outcomes.