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Dental considerations for patients with Hunter syndrome

Authors
 Da-Young Cho  ;  Kyung-Hyun Cho  ;  Je Seon Song  ;  Seong-Oh Kim 
Citation
 International Journal of Disability and Oral Health, Vol.17(1) : 10-14, 2021-06 
Journal Title
International Journal of Disability and Oral Health
ISSN
 2713-7759 
Issue Date
2021-06
Keywords
Hunter syndrome ; Mucopolysaccharidosis type II ; Iduronate-2-sulfatase
Abstract
Hunter syndrome, or mucopolysaccharidosis type II, is a rare X-linked disorder caused by a deficiency in the lysosomal enzyme iduronate-2-sulfatase. This results in accumulation of glycosaminoglycans (GAGs) in the lysosomes of various tissues. It causes physical and mental degeneration, in severe cases, death during the teenage years. Dental complications include enamel hypoplasia, microdontia, dentigerous cyst-like follicles, unerupted dentition, malocclusions, gingival hyperplasia, macroglossia, and condylar defects. This is a case report of a 9-year-old boy who visited the Dentistry Department of Pediatric Dentistry, Yonsei University Dental Hospital with a chief complaint of over-all dental treatment and bruxism. This report discusses oral manifestations of Hunter syndrome and its dental management methods
Full Text
https://www.dbpia.co.kr/journal/articleDetail?nodeId=NODE10600663
Appears in Collections:
2. College of Dentistry (치과대학) > Dept. of Pediatric Dentistry (소아치과학교실) > 1. Journal Papers
Yonsei Authors
Kim, Seong Oh(김성오) ORCID logo https://orcid.org/0000-0002-8620-1377
Song, Je Seon(송제선) ORCID logo https://orcid.org/0000-0001-8620-5629
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/187298
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