18 51

Cited 0 times in

Lesch-Nyhan syndrome환아의 oral self-mutilation에 대한 증례보고

Other Titles
 ORAL SELF-MUTILATION IN THE LESCH-NYHAN SYNDROME : CASE REPORT 
Authors
 전진용  ;  이제호  ;  최형준  ;  최병재 
Citation
 Journal of the Korean Academy of Pediatric Dentistry (대한소아치과학회지), Vol.26(1) : 151-156, 1999 
Journal Title
 Journal of the Korean Academy of Pediatric Dentistry (대한소아치과학회지) 
ISSN
 1226-8496 
Issue Date
1999
Keywords
LESCH-NYHAN SYNDROME ; ORAL SELF-MUTILATION ; self-injurious behavior ; self-mutilation
Abstract
Self-injurious behavior is defined as deliberate harm to one's own body without suicidal intent. It usually occurs as head banging or hitting, skin cutting, or finger biting and includes ocular, genital and oral self-mutilation. Lesch-Nyhan syndrome is a rare X-linked recessively inherited disorder, caused by complete absence of hypoxanthin-guanine phosphoribosyl transferase(HPRT) activity. Clinical presentation is characterized by mental retardation, chorea, athetosis, hyperuricemia, uricosuria and self-mutilating behavior. In these patients, the most typical feature is loss of tissue from biting themselves, even though they are not insensitive to pain. The dental management of self-mutilation includes treatment with appliances such as soft mouthguard or lip bumper, extraction of all the teeth, and orthognathic surgery. We report a 25-month-old boy who was a known case of Lesch-Nyhan syndrome and presented with severe self-mutilation wound on his lower lip. Vital pulpectomy and coronal resection was done as a more conservative approach than extracting all primary anterior teeth. Due to maintaining the root portion of the teeth in the bone, it is expected that the normal growth of the alveolar bone will be achieved.
Files in This Item:
T199902394.pdf Download
Appears in Collections:
2. College of Dentistry (치과대학) > Dept. of Pediatric Dentistry (소아치과학교실) > 1. Journal Papers
Yonsei Authors
Choi, Byung Jai(최병재)
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/172781
사서에게 알리기
  feedback

qrcode

Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.

Browse