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구순구개열 및 가로얼굴파열을 동반한 Goldenhar Syndrome 환자에서 수술적 치료: 증례보고

Other Titles
 Surgical Treatment of a Goldenhar Syndrome Patient with Cleft Lip and Palate and Transverse Facial Cleft: Case Report 
Authors
 박종열  ;  김준영  ;  박진후  ;  정휘동  ;  정영수 
Citation
 Korean Journal of Cleft Lip and Palate Association (대한구순구개열학회지), Vol.22(1) : 21-26, 2019-06 
Journal Title
 Korean Journal of Cleft Lip and Palate Association (대한구순구개열학회지) 
ISSN
 1229-0734 
Issue Date
2019-06
Keywords
Goldenhar syndrome ; Hemifacial microsomia ; Macrostomia ; Cleft lip and palate ; Transverse facial cleft Goldenhar syndrome ; Hemifacial microsomia ; Macrostomia ; Cleft lip and palate ; Transverse facial cleft
Abstract
Goldenhar syndrome is also knowns as Oculo-Auriculo-Vertebral Syndrome which is a rare case. It represents hemifacial microsomia, macrostomia and cleft lip and palate (CLP) in facial characteristics. It has a wide range of multiple symptoms in ophthalmic, auricular, skeletal, vertebral and cardiac system. Though the etiology of this syndrome is not fully understood, it has shown variable characteristics which are caused by uncertain factors. The incidence of this syndrome ranges from 1 in 35,000 to 56,000. The treatment within an appropriate time is able to increase the chances of a good prognosis. In this paper, we report a case of patient with Goldenhar syndrome showing macrostomia and CLP. This patient underwent two surgeries; firstly, the primary lip and nose repair for unilateral complete lip and palate, secondly, the commissure repair of transverse facial cleft and skin excision of preauricular tag. Herein we continue to emphasize the necessity of proper surgery technique along with a timely treatment in conjunction with multidisciplinary management of systemic abnormalities.
Files in This Item:
T201906301.pdf Download
DOI
10.31136/kjclp.2019.22.1.21
Appears in Collections:
2. College of Dentistry (치과대학) > Dept. of Oral and Maxillofacial Surgery (구강악안면외과학교실) > 1. Journal Papers
Yonsei Authors
Kim, Jun-Young(김준영) ORCID logo https://orcid.org/0000-0002-6596-6135
Park, Jin Hoo(박진후) ORCID logo https://orcid.org/0000-0003-2337-9554
Jung, Young Soo(정영수) ORCID logo https://orcid.org/0000-0001-5831-6508
Jung, Hwi Dong(정휘동) ORCID logo https://orcid.org/0000-0003-1025-8323
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/175912
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