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구척수근위축증에서 감각신경병의 단면적 및 종적 연구

 김지영  ;  박기덕  ;  김승민  ;  선우일남 
 Journal of the Korean Association of EMG-Electrodiagnostic Medicine (대한근전도 전기진단의학회지), Vol.16(1) : 20-23, 2014 
Journal Title
Journal of the Korean Association of EMG-Electrodiagnostic Medicine(대한근전도 전기진단의학회지)
Issue Date
Bulbospinal muscular atrophy ; Neuronopathy ; Sensory ; Action potentials
Objectives: Bulbo-spinal muscular atrophy (BSMA) is an inherited motor neuronopathy, but it is known that subclinical sensory neuropathy can be found. The objective of this study is to clarify the features of sensory neuropathy by cross-sectional and longitudinal studies. Method: We analyzed the clinical and electrodiagnostic data of 41 BSMA patients who were genetically confirmed. Follow-up studies were performed in 10 patients among them. Results: Of 41 patients, 11 complained of sensory symptoms (26.8%), such as numbness or paresthesia of distal extremities. However, sensory neuropathy was observed in 23 patients (56.1%) with nerve conduction study (NCS). Reduced amplitude of action potentials was the most remarkable finding of the group with sensory neuropathy. For 10 patients with follow-up NCS, the mean follow-up interval was 8 years. There was no significant temporal change between the first and the follow-up sensory NCS. Conclusion: Subclinical sensory neuropathy was found in 56.1% of BSMA patients. The longitudinal study shows that subclinical sensory neuropathy in BSMA may not progress over time.
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1. College of Medicine (의과대학) > Dept. of Neurology (신경과학교실) > 1. Journal Papers
Yonsei Authors
Kim, Seung Min(김승민) ORCID logo https://orcid.org/0000-0002-4384-9640
Sunwoo, Il Nam(선우일남)
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