신경근육질환 환자에서 비침습적 호흡기 사용 경과 고찰

Abstract

Objective: To report an overall survey of the application state of non-invasive intermittent positive pressure ventilator (NIPPV) in patients with neuromuscular diseases who were managed successfully in this hospital. Method: To estimate current state of NIPPV application, chart review and telephone survey were performed in neuromuscular patients who applied NIPPV successfully from March 2001 to January 2006 in this hospital. Results: Among 161 patients who once tried NIPPV, 100 patients applied NIPPV successfully. The composition was 66 patients with myopathy, 20 patients with amyotrophic lateral scoliosis, 6 patients with spinal muscular atrophy, 3 patients with cervical cord injury, and 5 patients with other neuromuscular diseases. Among them, 12 patients who had undertaken tracheostomy were switched into NIPPV, however 3 ALS paients who had first applied NIPPV successfully were taken tracheostomy later. Conclusion: NIPPV is an equally effective and safe tool for ventilatory support, which can be used as an alternative method of invasive ventilatory support for patients with advanced neuromuscular diseases. We assume that more neuromuscular patients can improve their quality of life, and prolong their life span through application of NIPPV.