Successful Heart Transplant in Dilated Cardiomyopathy Associated With Alstro euro m Syndrome: A Case Report

Abstract

Alstro euro m syndrome is a rare, multisystemic genetic disorder, and dilated cardiomyopathy occurs in approximately two-thirds of patients with this condition. Because of donor organ shortage and unfavorable prognosis of multiple organ dysfunction, heart transplant is not the most desirable therapeutic option for patients with dilated cardiomyopathy with Alstro euro m syndrome. However, eliminating heart dysfunction elements at an appropriate time itself plays a pivotal role in pre -venting or even reversing other organ failures. Herein, we report the case of a 17-year-old boy who underwent successful isolated heart transplant despite severe liver dysfunction.