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Successful Heart Transplant in Dilated Cardiomyopathy Associated With Alström Syndrome: A Case Report

Authors
 Jung Min Park  ;  Yu Rim Shin  ;  Jae Won Oh  ;  Jo Won Jung 
Citation
 TRANSPLANTATION PROCEEDINGS, Vol.54(10) : 2800-2802, 2022-12 
Journal Title
TRANSPLANTATION PROCEEDINGS
ISSN
 0041-1345 
Issue Date
2022-12
MeSH
Adolescent ; Alstrom Syndrome* / complications ; Alstrom Syndrome* / diagnosis ; Alstrom Syndrome* / genetics ; Cardiomyopathies* / complications ; Cardiomyopathy, Dilated* / complications ; Cardiomyopathy, Dilated* / surgery ; Heart Transplantation* ; Humans ; Male
Abstract
Alström syndrome is a rare, multisystemic genetic disorder, and dilated cardiomyopathy occurs in approximately two-thirds of patients with this condition. Because of donor organ shortage and unfavorable prognosis of multiple organ dysfunction, heart transplant is not the most desirable therapeutic option for patients with dilated cardiomyopathy with Alström syndrome. However, eliminating heart dysfunction elements at an appropriate time itself plays a pivotal role in preventing or even reversing other organ failures. Herein, we report the case of a 17-year-old boy who underwent successful isolated heart transplant despite severe liver dysfunction.
Full Text
https://www.sciencedirect.com/science/article/pii/S0041134522006881
DOI
10.1016/j.transproceed.2022.09.028
Appears in Collections:
1. College of Medicine (의과대학) > Dept. of Internal Medicine (내과학교실) > 1. Journal Papers
1. College of Medicine (의과대학) > Dept. of Pediatrics (소아과학교실) > 1. Journal Papers
1. College of Medicine (의과대학) > Dept. of Thoracic and Cardiovascular Surgery (흉부외과학교실) > 1. Journal Papers
Yonsei Authors
Shin, Yu Rim(신유림)
Oh, Jae Won(오재원) ORCID logo https://orcid.org/0000-0002-4585-1488
Jung, Jo Won(정조원)
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/192999
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