Neurilemmoma is a benign encapsulated tumor which originates from any nerve covered with a Schwann cell sheath. Therefore, it can arise from the peripheral nerves, spinal nerve roots as well as all cranial nerves except the olfactory and optic nerves which do not possess such sheaths. It is a characteristically benign, solitary and well-encapsulated mass. About 25% of neurilemmoma occurs in the head and neck region and the vestibular nerve is most frequently involved. But its occurrence in the larynx is extremely rare. Recently, the authors have experienced a case of neurilemmoma originated from the larynx in a 46 year old male patient. The tumor was successfully removed through external approach under general anesthesia and it was histologically proven as a neruilemmoma.