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Precise Pulmonary Function Evaluation and Management of a Patient With Freeman-Sheldon Syndrome Associated With Recurrent Pneumonia and Chronic Respiratory Insufficiency

DC Field Value Language
dc.contributor.author강성웅-
dc.contributor.author박지현-
dc.contributor.author조한얼-
dc.contributor.author최원아-
dc.date.accessioned2020-12-01T17:16:16Z-
dc.date.available2020-12-01T17:16:16Z-
dc.date.issued2020-04-
dc.identifier.issn2234-0645-
dc.identifier.urihttps://ir.ymlib.yonsei.ac.kr/handle/22282913/180193-
dc.description.abstractFreeman-Sheldon syndrome (FSS) is a rare distal arthrogryposis syndrome. There are few reports on the respiratory insufficiency of FSS. Additionally, there is no detailed information on pulmonary functional evaluation. A 17-year-old male patient with FSS developed respiratory failure, leading him to be admitted to hospital several times for evaluation and treatment. Of those times he was admitted, two were due to pneumonia. His pulmonary functions were indicative of a restrictive lung disease potentially caused by severe scoliosis. After a non-invasive ventilatorwas applied correctly to the patient, pulmonary hypertension was normalized. His pulmonary function has been maintained for 13 years. Since receiving proper respiratory care, which includes assisted coughing methods, the patient has not developed pneumonia. It is important to properly evaluate the pulmonary function of patients who have FSS and scoliosis to eliminate the risk of long-term respiratory complications.-
dc.description.statementOfResponsibilityopen-
dc.languageEnglish-
dc.publisherKorean Academy of Rehabilitation Medicine-
dc.relation.isPartOfAnnals of Rehabilitation Medicine-
dc.rightsCC BY-NC-ND 2.0 KR-
dc.titlePrecise Pulmonary Function Evaluation and Management of a Patient With Freeman-Sheldon Syndrome Associated With Recurrent Pneumonia and Chronic Respiratory Insufficiency-
dc.typeArticle-
dc.contributor.collegeCollege of Medicine (의과대학)-
dc.contributor.departmentDept. of Rehabilitation Medicine (재활의학교실)-
dc.contributor.googleauthorJihyun Park-
dc.contributor.googleauthorSeong-Woong Kang-
dc.contributor.googleauthorWon Ah Choi-
dc.contributor.googleauthorYewon Lee-
dc.contributor.googleauthorHan Eol Cho-
dc.identifier.doi10.5535/arm.2020.44.2.165-
dc.contributor.localIdA00041-
dc.contributor.localIdA05337-
dc.contributor.localIdA05854-
dc.contributor.localIdA04125-
dc.relation.journalcodeJ00177-
dc.identifier.eissn2234-0653-
dc.identifier.pmid32392656-
dc.subject.keywordFreeman-Sheldon syndrome-
dc.subject.keywordRespiratory function tests-
dc.subject.keywordRespiratory insufficiency-
dc.contributor.alternativeNameKang, Seong Woong-
dc.contributor.affiliatedAuthor강성웅-
dc.contributor.affiliatedAuthor박지현-
dc.contributor.affiliatedAuthor조한얼-
dc.contributor.affiliatedAuthor최원아-
dc.citation.volume44-
dc.citation.number2-
dc.citation.startPage165-
dc.citation.endPage170-
dc.identifier.bibliographicCitationAnnals of Rehabilitation Medicine, Vol.44(2) : 165-170, 2020-04-
dc.identifier.rimsid67499-
dc.type.rimsART-
Appears in Collections:
1. College of Medicine (의과대학) > Dept. of Rehabilitation Medicine (재활의학교실) > 1. Journal Papers

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