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수포성 표피박리증을 동반한 선천성 유문폐쇄증 1예

Other Titles
 Congenital Pyloric Atresia with Junctional Epidermolysis Bullosa: a Case Report 
Authors
 조마해  ;  한석주 
Citation
 Journal of the Korean Association of Pediatric Surgeons (소아외과), Vol.3(1) : 77-82, 1997 
Journal Title
 Journal of the Korean Association of Pediatric Surgeons (소아외과) 
ISSN
 1225-9047 
Issue Date
1997
MeSH
Blister ; Epidermolysis Bullosa ; Epidermolysis Bullosa, Junctional* ; Female ; Humans ; Infant, Newborn ; Microscopy ; Microscopy, Electron ; Mouth Mucosa ; Parturition ; Radiography ; Skin
Keywords
Pyloric atresia ; Epidermolysis bullosa
Abstract
The association of pyloric atresia and epidermolysis bullosa(EB) in newborn is rare and inheritant as an autosomal recessive trait. We report a newborn girl with pyloric atresia and epidermolysis bullosa. Blisters were noted on her skin at birth, especially in pressure-exposed area, and later on the oral mucosa. Junctional epidermolysis bullosa was confirmed by light microscopy and electron microscopy. Radiography revealed pyloric atresia. Segmental resection of 1.5 cm and gastroduodenostomy were carried out at 4 days of age. Protein loosing enteropathy developed after oral feeding. The frequency of episodes of nonscarred blisters and the severity and duration improved significantly with time. The protein loosing enteropathy was persistent, and at 1 year of age, her growth is markedly retarded.
Full Text
https://www.aps-journal.org/search.php?where=aview&id=10.13029/jkaps.1997.3.1.77&code=0053JKAPS&vmode=FULL
DOI
10.13029/jkaps.1997.3.1.77
Appears in Collections:
1. College of Medicine (의과대학) > Dept. of Surgery (외과학교실) > 1. Journal Papers
Yonsei Authors
Han, Seok Joo(한석주) ORCID logo https://orcid.org/0000-0001-5224-1437
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/177674
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