0 186

Cited 7 times in

Bilateral globus pallidus interna deep-brain stimulation in a patient with myoclonus-dystonia: a case report.

Authors
 Ji Hee Kim  ;  Young Cheol Na  ;  Won Hee Lee  ;  Won Seok Chang  ;  Hyun Ho Jung  ;  Jin Woo Chang 
Citation
 NEUROMODULATION, Vol.17(8) : 724-728, 2014 
Journal Title
 NEUROMODULATION 
ISSN
 1094-7159 
Issue Date
2014
MeSH
Adult ; Deep Brain Stimulation/methods* ; Disability Evaluation ; Dystonic Disorders/therapy* ; Female ; Functional Laterality/physiology* ; Globus Pallidus/physiology* ; Humans
Keywords
Deep brain stimulation ; dystonia ; globus pallidus interna ; myoclonus ; myoclonus-dystonia
Abstract
OBJECTIVE: Myoclonus-dystonia is a movement disorder characterized by childhood onset of myoclonus and dystonia. We report a case of the epsilon-sarcoglycan mutation-negative myoclonus-dystonia patient who underwent bilateral globus pallidus interna deep-brain stimulation with subsequent improvement of both myoclonus and dystonia. CASE REPORT: A 37-year-old woman with myoclonic jerks and dystonia affecting predominantly the lower limbs was treated with chronic bilateral globus pallidus interna deep-brain stimulation. RESULTS: The movement subscore of the Burke-Fahns-Marsden Dystonia Rating Scale was 38 before surgery and improved to 7 after 3 years. The disability subscore of the Burke-Fahns-Marsden Dystonia Rating Scale improved from 7 to 2. The Unified Myoclonus Rating Scale also decreased significantly from 93 to 39. No hardware- or stimulation-related complications occurred during follow-up. CONCLUSION: This report suggests that patients with myoclonus-dystonia may significantly benefit from bilateral globus pallidus interna deep-brain stimulation. Larger studies of this patient population are needed to confirm the optimal target.
Full Text
http://onlinelibrary.wiley.com/doi/10.1111/ner.12162/abstract
DOI
10.1111/ner.12162
Appears in Collections:
1. College of Medicine (의과대학) > Dept. of Neurosurgery (신경외과학교실) > 1. Journal Papers
Yonsei Authors
Na, Young Chul(나영철)
Chang, Won Seok(장원석) ORCID logo https://orcid.org/0000-0003-3145-4016
Chang, Jin Woo(장진우) ORCID logo https://orcid.org/0000-0002-2717-0101
Jung, Hyun Ho(정현호)
URI
https://ir.ymlib.yonsei.ac.kr/handle/22282913/138633
사서에게 알리기
  feedback

qrcode

Items in DSpace are protected by copyright, with all rights reserved, unless otherwise indicated.

Browse