낭성 부분분화신모세포종 1례

Abstract

Cystic partially differentiated nephroblastoma is a rare renal mass in children. Since its clinical characteristics and radiologic findings are very similar to those of cystic Wilms tumor and cystic nephroma, the discrimination between these disease categories are known to be difficult and only possible by histology. A 9-month-old female presented with 2 months history of abdominal distension. Renal ultrasonography showed a mass with multiple cystic components in the upper to lower poles of the right kidney and computer tomography showed a well-marginated low attenuation multilocular cystic mass. Right nephrectomy was performed and cystic partially differentiated nephroblastoma was diagnosed by pathologic findings. There have been only few reports in the literature with only one case report in Korea. Here we report a case of cystic partially differentiated nephroblastoma with some review of the literatures