후복막에 발생한 원발성 점액성낭선암종 1예

Abstract

Primary retroperitoneal mucinous cystadenocarinoma is extremely rare with only five case reported in the literature. Primary mucinous adenocarcinoma is apparent that a primary retroperitoneal process in development results in tissue susceptible to malignants degeneration. It is impossible to clarify the precise defect in embryologic growth that allows these tumors to develop. The theory of coelomic metaplasia has gained increasing support in recent years for origin of the epithelial neoplasms of the ovary, and an invagination of the same coelomic or pertioneal epithelial layer with concurrent or subsqeunt metaplasia account for retroperitoneal mucinous neoplasms The preoperative course of these cysts appears indolent, yet the eoveall prognosis is poor. The role of chemotherapy in the treatment of these tumors remains undrfined. colse follow-up and aggressive management based on histologic appearance are indicated to improve the outcome of the patients with retroperitoneal mucinous cystadenocarinoam. Recently, We repoorted one case of primary retroperitoneal nucinous cytadeno -carcioma. The patient was a 32 year-old female complaing a palpable mass and discomfort in the left flank. Laparotomy revealed a huge retroperitoneal mass in the presence of bilateral normal ovaries. Histologically, it was a mucinous cystic neoplasm with flankly malignat area. No ovarian issue was found din the mass.