피부 궤양을 동반한 성인형 피부근염 1예

Abstract

Dermatomyositis (DM) is a connective tissue disorder characterized by inflammatory myopathy and prominent cutaneous features. Although cutaneous vasculitis has been noted frequently in child onset DM, it rarely occurs in adult-onset DM. The clinical features of adult-onset DM showing cutaneous vasculitis have not been well characterized. A 60-year-old female patient presented with multiple deep cutaneous ulcers in both hands, elbows and foot. She was diagnosed as dermatomyositis 18 months before admission. Angiogram showed no definite arterial obstructive lesion and thrombus in both wrist and elbow, but decreased vascularity was seen in digits of both hands. Cutaneous ulceration was thought to be caused by vasculitis. Cutaneous ulceration was a rare manifestation of adult-onset DM patients, and we report this case with a review of literature.