Background Nevus comedonicus is an uncommon malformation of the pilosebaceous unit. Association of nevus comedonicus with tumors originating from the apocrine gland has not previously been reported.
Method We present a case of nevus comedonicus associated with hidradenoma papilliferum (HAP) and syringocystadenoma papilliferum (SCAP) in the female genital area.
Results Histological features strongly suggested nevus comedonicus associated with HAP and SCAP.
Conclusion Although the association of nevus comedonicus with HAP and SCAP is very rare, the possibility of coexistence cannot be excluded.