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난치성 간질을 동반한 Parry-Romberg 증후군 1례
DC Field | Value | Language |
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dc.contributor.author | 송동호 | - |
dc.date.accessioned | 2015-07-15T16:52:04Z | - |
dc.date.available | 2015-07-15T16:52:04Z | - |
dc.date.issued | 2003 | - |
dc.identifier.issn | 1226-6884 | - |
dc.identifier.uri | https://ir.ymlib.yonsei.ac.kr/handle/22282913/113756 | - |
dc.description.abstract | Parry-Romberg syndrome, first described in 1825 by Parry and in 1846 by Romberg, is a rare disorder characterized by a progressive hemifacial atrophy of the skin and adipose tissue and atrophy of muscle, cartilage, and underlying bony structures. It is sometimes accompanied with such complications as ophthalmologic abnormality, localized alopecia and neurologic symptoms, for example, contralateral Jacksonian epilepsy, trigeminal neuralgia, migrane and hemiplegia. The onset is slow and progressive, starting at the first or second decade of life and lasting for 2-10 years, ending with a face being 'burned out'. It is often associated with epilepsy but the link between these two conditions is poorly understood. In patients with progressive hemifacial atrophy, a high incidence of abnormal neuroradiologic findings in the brain has been reported. Brain MRI findings include cerebral hemiatrophy, cortical calcification, unilateral focal infarction in the corpus callosum, diffuse deep and subcortical white matter signal changes and mild cortical thickening. We report a case of Parry-Romberg syndrome in a 5-year-old boy who had a progressive Rt. facial hemiatrophy with intractable epilepsy and basal ganglia calcification from brain MRI. | - |
dc.description.statementOfResponsibility | open | - |
dc.language | Korean | - |
dc.publisher | 대한소아신경학회 | - |
dc.relation.isPartOf | Journal of the Korean Child Neurology Society | - |
dc.rights | CC BY-NC-ND 2.0 KR | - |
dc.rights.uri | https://creativecommons.org/licenses/by-nc-nd/2.0/kr/ | - |
dc.subject.MESH | Progressive hemifacial atrophy | - |
dc.subject.MESH | Parry-Romberg syndrome | - |
dc.subject.MESH | Intractable seizure | - |
dc.title | 난치성 간질을 동반한 Parry-Romberg 증후군 1례 | - |
dc.title.alternative | A Case of Parry-Romberg Syndrome with Intractable Seizure | - |
dc.type | Article | - |
dc.contributor.college | College of Medicine (의과대학) | - |
dc.contributor.department | Dept. of Psychiatry (정신과학) | - |
dc.contributor.googleauthor | 허윤정 | - |
dc.contributor.googleauthor | 김성우 | - |
dc.contributor.googleauthor | 정희정 | - |
dc.contributor.googleauthor | 송동우 | - |
dc.admin.author | false | - |
dc.admin.mapping | false | - |
dc.contributor.localId | A02018 | - |
dc.relation.journalcode | J01815 | - |
dc.identifier.url | http://scholar.dkyobobook.co.kr/searchDetail.laf?barcode=4010022737848 | - |
dc.subject.keyword | Progressive hemifacial atrophy | - |
dc.subject.keyword | Parry-Romberg syndrome | - |
dc.subject.keyword | Intractable seizure | - |
dc.contributor.alternativeName | Song, Dong Ho | - |
dc.contributor.affiliatedAuthor | Song, Dong Ho | - |
dc.rights.accessRights | not free | - |
dc.citation.volume | 11 | - |
dc.citation.number | 1 | - |
dc.citation.startPage | 144 | - |
dc.citation.endPage | 149 | - |
dc.identifier.bibliographicCitation | Journal of the Korean Child Neurology Society, Vol.11(1) : 144-149, 2003 | - |
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