방광에서 발생한 악성 근주위세포종

Abstract

A myopericytoma is a rare benign neoplasm, which shows perivascular growth of the spindle cells and their differentiation to perivascular myoid cells. Several tumors, showing such histological findings, including myopericytomas, glomangiopericytomas, solitary myofibromas and infantile hemangiopericytomas, were previously named hemangiopericytomas. However, they are now regarded as the same group of disease, with similar histological findings. Such tumors usually originate in the subcutaneous tissue of the extremities, but very rarely originate in visceral organs. Until now, only 7 cases originating in the urinary bladder have previously been reported as hemangiopericytomas. Although macroscopically the aspect is benign, it has a recognized ability for local invasion and distant dissemination. Radical surgical excision is the treatment of choice, as adjuvant chemotherapy and radiation therapy offer limited success in this malignancy. A case of a 57 year-old woman with a malignant myopericytoma, originating in the urinary bladder, with extensive lung metastasis, is reported.