A sinonasal inverted papilloma is a benign tumor which has been reported up to 4%. However, an inverted papilloma originating in the sphenoid sinus is even rarer, and a pediatric case has never before been reported. We report a case of pediatric inverted papilloma originating in the sphenoid sinus that presented with symptoms of sinusitis. Endoscopic sinus surgery was performed using a computer-aided image-guided system. The tumor was removed without any surgical complications or recurrence for 2 years