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Pediatric cervical chordoma: report of two cases and a review of the current literature

 Gwi Hyun Choi  ;  Moon-Sool Yang  ;  Do Heum Yoon  ;  Hyun Chyul Shin  ;  Keung Nyun Kim  ;  Seong Yi  ;  Dong Yeop Lee  ;  Poong Gi Ahn  ;  Yoon Ha 
 Child's Nervous System, Vol.26(6) : 835-840, 2010 
Journal Title
 Child's Nervous System 
Issue Date
Cervical Vertebrae ; Child ; Chordoma/pathology ; Chordoma/radiotherapy* ; Chordoma/surgery* ; Combined Modality Therapy/methods ; Follow-Up Studies ; Humans ; Immunohistochemistry ; Magnetic Resonance Imaging ; Male ; Neurosurgical Procedures/methods ; Protons/therapeutic use ; Radiography ; Spinal Cord/diagnostic imaging ; Spinal Cord/metabolism ; Spinal Cord/surgery ; Spinal Cord Neoplasms/pathology ; Spinal Cord Neoplasms/radiotherapy* ; Spinal Cord Neoplasms/surgery* ; Treatment Outcome
Chordoma ; Cervical spine ; Childhood
INTRODUCTION: The majority of chordomas occur between the fifth and seventh decades of life and are thus extremely rare in children, which account for less than 5% of all spinal chordoma cases. CASE REPORT: We report on the development of this rare condition in two boys aged 7 and 10 years. One patient presented with a palpable neck mass and dysphagia, while the other presented with posterior neck pain. Radiological studies revealed an extensive mass in the cervical vertebrae and paravertebral soft tissue of both patients. The tumors were subtotally removed in an attempt to improve the success of adjuvant proton beam radiotherapy. Pathological examination, which included immunohistochemical staining, revealed chordoma of the cervical spine in both patients. CONCLUSION: Although en bloc resection is the ideal modality for treatment of chordoma, such a procedure is often associated with a significant risk of surgical morbidity due to the tumor location. Therefore, piecemeal resection followed by postoperative adjuvant radiotherapy, including proton radiotherapy or radiosurgery, should be considered in such cases.
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1. College of Medicine (의과대학) > Dept. of Neurosurgery (신경외과학교실) > 1. Journal Papers
Yonsei Authors
Kim, Keung Nyun(김긍년)
Ahn, Poong Gee(안풍기)
Yang, Moon Sool(양문술)
Yoon, Do Heum(윤도흠) ORCID logo https://orcid.org/0000-0003-1452-5724
Lee, Dong Yup(이동엽)
Yi, Seong(이성)
Choi, Gwi Hyun(최귀현)
Ha, Yoon(하윤)
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